Chapter III
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
(D50-D89)
Coagulation defects, purpura and other haemorrhagic conditions
(D65-D69)
D65 | Disseminated intravascular coagulation [defibrination syndrome] Latin: Coagulatio intravascularis disseminata | |||||||
Afibrinogenaemia, acquired Consumption coagulopathy Diffuse or disseminated intravascular coagulation[DIC] Fibrinolytic haemorrhage, acquired Purpura: · fibrinolytic · fulminans | ||||||||
Excludes: | that (complicating): · abortion or ectopic or molar pregnancy (O00-O07, O08.1) · in newborn (P60) · pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3) |
D66 | Hereditary factor VIII deficiency Latin: Haemophilia A propter deficientiam factoris VIII | |||||||
Deficiency factor VIII (with functional defect) Haemophilia: · NOS · A · classical | ||||||||
Excludes: | factor VIII deficiency with vascular defect (D68.0) |
D67 | Hereditary factor IX deficiency Latin: Haemophilia B propter deficientiam factoris IX | |||||||
Christmas disease Deficiency: · factor IX (with functional defect) · plasma thromboplastin component [PTC] Haemophilia B |
D68 | Other coagulation defects Latin: Defectus coagulationis alii | |||||||
Excludes: | those complicating: · abortion or ectopic or molar pregnancy (O00-O07, O08.1) · pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3) | |||||||
D68.0 | Von Willebrand's disease Latin: Morbus von Willebrand | |||||||
Angiohaemophilia Factor VIII deficiency with vascular defect Vascular haemophilia | ||||||||
Excludes: | capillary fragility (hereditary) (D69.8) factor VIII deficiency: · NOS (D66) · with functional defect (D66) | |||||||
D68.1 | Hereditary factor XI deficiency Latin: Deficientia factoris IX hereditaria | |||||||
Haemophilia C Plasma thromboplastin antecedent [PTA] deficiency | ||||||||
D68.2 | Hereditary deficiency of other clotting factors Latin: Deficientia factorum coagulationis aliorum hereditaria | |||||||
Congenital afibrinogenaemia Deficiency: · AC globulin · proaccelerin Deficiency of factor: · I [fibrinogen] · II [prothrombin] · V [labile] · VII [stable] · X [Stuart-Prower] · XII [Hageman] · XIII [fibrin-stabilizing] Dysfibrinogenaemia (congenital) Hypoproconvertinaemia Owren's disease | ||||||||
D68.3 | Haemorrhagic disorder due to circulating anticoagulants Latin: Disordo haemorrhagicus propter anticoagulantes circulatorios | |||||||
Haemorrhage during long-term use of anticoagulants Hyperheparinaemia Increase in: · antithrombin · anti-VIIIa · anti-IXa · anti-Xa · anti-XIa | ||||||||
Use additional external cause code (Chapter XX), if desired, to identify any administered anticoagulant. | ||||||||
Excludes: | long-term use of anticoagulants without haemorrhage (Z92.1) | |||||||
D68.4 | Acquired coagulation factor deficiency Latin: Deficientia factoris coagulationis acquisita | |||||||
Deficiency of coagulation factor due to: · liver disease · vitamin K deficiency | ||||||||
Excludes: | vitamin K deficiency of newborn (P53) | |||||||
D68.8 | Other specified coagulation defects Latin: Defectus coagulationis specificati alii | |||||||
Presence of systemic lupus erythematosus [SLE] inhibitor | ||||||||
D68.9 | Coagulation defect, unspecified Latin: Defectus coagulationis, non specificatus |
D69 | Purpura and other haemorrhagic conditions Latin: Purpura et status haemorrhagici alii | |||||||
Excludes: | benign hypergammaglobulinaemic purpura (D89.0) cryoglobulinaemic purpura (D89.1) essential (haemorrhagic) thrombocythaemia (D47.3) purpura fulminans (D65) thrombotic thrombocytopenic purpura (M31.1) | |||||||
D69.0 | Allergic purpura Latin: Purpura allergica | |||||||
Purpura: · anaphylactoid · Henoch(-Schönlein) · nonthrombocytopenic: · haemorrhagic · idiopathic · vascular Vasculitis, allergic | ||||||||
D69.1 | Qualitative platelet defects Latin: Defectus trombocytorum qualitativi | |||||||
Bernard-Soulier [giant platelet] syndrome Glanzmann's disease Grey platelet syndrome Thromboasthenia (haemorrhagic)(hereditary) Thrombocytopathy | ||||||||
Excludes: | von Willebrand's disease (D68.0) | |||||||
D69.2 | Other nonthrombocytopenic purpura Latin: Purpura non thrombocytopenica alia | |||||||
Purpura: · NOS · senile · simplex | ||||||||
D69.3 | Idiopathic thrombocytopenic purpura Latin: Purpura thrombocytopenica idiopathica | |||||||
Evans' syndrome | ||||||||
D69.4 | Other primary thrombocytopenia Latin: Thrombocytopenia primaria alia | |||||||
Excludes: | thrombocytopenia with absent radius (Q87.2) transient neonatal thrombocytopenia (P61.0) Wiskott-Aldrich syndrome (D82.0) | |||||||
D69.5 | Secondary thrombocytopenia Latin: Thrombocytopenia secundaria | |||||||
Use additional external cause code (Chapter XX), if desired, to identify cause. | ||||||||
D69.6 | Thrombocytopenia, unspecified Latin: Thrombocytopenia, non specificata | |||||||
D69.8 | Other specified haemorrhagic conditions Latin: Status haemorrhagici specificati, alii | |||||||
Capillary fragility (hereditary) Vascular pseudohaemophilia | ||||||||
D69.9 | Haemorrhagic condition, unspecified Latin: Status haemorrhagicus, non specificatus |
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