A00-B99 C00-D48D50-D89 E00-E90 F00-F99 G00-G99 H00-H59 H60-H95 I00-I99 J00-J99 K00-K93
L00-L99 M00-M99 N00-N99 O00-O99 P00-P96 Q00-Q99 R00-R99 S00-T98 V01-Y98 Z00-Z99 U00-U99

D65-D69 Coagulation defects, purpura and other haemorrhagic conditions

Chapter III

Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

Coagulation defects, purpura and other haemorrhagic conditions

D65Disseminated intravascular coagulation [defibrination syndrome]
Latin: Coagulatio intravascularis disseminata
Afibrinogenaemia, acquired
Consumption coagulopathy
Diffuse or disseminated intravascular coagulation[DIC]
Fibrinolytic haemorrhage, acquired
· fibrinolytic
· fulminans
Excludes:that (complicating):
· abortion or ectopic or molar pregnancy (O00-O07, O08.1)
· in newborn (P60)
· pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)

D66Hereditary factor VIII deficiency
Latin: Haemophilia A propter deficientiam factoris VIII
Deficiency factor VIII (with functional defect)
· A
· classical
Excludes:factor VIII deficiency with vascular defect (D68.0)

D67Hereditary factor IX deficiency
Latin: Haemophilia B propter deficientiam factoris IX
Christmas disease
· factor IX (with functional defect)
· plasma thromboplastin component [PTC]
Haemophilia B

D68Other coagulation defects
Latin: Defectus coagulationis alii
Excludes:those complicating:
· abortion or ectopic or molar pregnancy (O00-O07, O08.1)
· pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
D68.0Von Willebrand's disease
Latin: Morbus von Willebrand
Factor VIII deficiency with vascular defect
Vascular haemophilia
Excludes:capillary fragility (hereditary) (D69.8)
factor VIII deficiency:
· NOS (D66)
· with functional defect (D66)
D68.1Hereditary factor XI deficiency
Latin: Deficientia factoris IX hereditaria
Haemophilia C
Plasma thromboplastin antecedent [PTA] deficiency
D68.2Hereditary deficiency of other clotting factors
Latin: Deficientia factorum coagulationis aliorum hereditaria
Congenital afibrinogenaemia
· AC globulin
· proaccelerin
Deficiency of factor:
· I [fibrinogen]
· II [prothrombin]
· V [labile]
· VII [stable]
· X [Stuart-Prower]
· XII [Hageman]
· XIII [fibrin-stabilizing]
Dysfibrinogenaemia (congenital)
Owren's disease
D68.3Haemorrhagic disorder due to circulating anticoagulants
Latin: Disordo haemorrhagicus propter anticoagulantes circulatorios
Haemorrhage during long-term use of anticoagulants
Increase in:
· antithrombin
· anti-VIIIa
· anti-IXa
· anti-Xa
· anti-XIa
Use additional external cause code (Chapter XX), if desired, to identify any administered anticoagulant.
Excludes:long-term use of anticoagulants without haemorrhage (Z92.1)
D68.4Acquired coagulation factor deficiency
Latin: Deficientia factoris coagulationis acquisita
Deficiency of coagulation factor due to:
· liver disease
· vitamin K deficiency
Excludes:vitamin K deficiency of newborn (P53)
D68.8Other specified coagulation defects
Latin: Defectus coagulationis specificati alii
Presence of systemic lupus erythematosus [SLE] inhibitor
D68.9Coagulation defect, unspecified
Latin: Defectus coagulationis, non specificatus

D69Purpura and other haemorrhagic conditions
Latin: Purpura et status haemorrhagici alii
Excludes:benign hypergammaglobulinaemic purpura (D89.0)
cryoglobulinaemic purpura (D89.1)
essential (haemorrhagic) thrombocythaemia (D47.3)
purpura fulminans (D65)
thrombotic thrombocytopenic purpura (M31.1)
D69.0Allergic purpura
Latin: Purpura allergica
· anaphylactoid
· Henoch(-Schönlein)
· nonthrombocytopenic:
  · haemorrhagic
  · idiopathic
· vascular
Vasculitis, allergic
D69.1Qualitative platelet defects
Latin: Defectus trombocytorum qualitativi
Bernard-Soulier [giant platelet] syndrome
Glanzmann's disease
Grey platelet syndrome
Thromboasthenia (haemorrhagic)(hereditary)
Excludes:von Willebrand's disease (D68.0)
D69.2Other nonthrombocytopenic purpura
Latin: Purpura non thrombocytopenica alia
· senile
· simplex
D69.3Idiopathic thrombocytopenic purpura
Latin: Purpura thrombocytopenica idiopathica
Evans' syndrome
D69.4Other primary thrombocytopenia
Latin: Thrombocytopenia primaria alia
Excludes:thrombocytopenia with absent radius (Q87.2)
transient neonatal thrombocytopenia (P61.0)
Wiskott-Aldrich syndrome (D82.0)
D69.5Secondary thrombocytopenia
Latin: Thrombocytopenia secundaria
Use additional external cause code (Chapter XX), if desired, to identify cause.
D69.6Thrombocytopenia, unspecified
Latin: Thrombocytopenia, non specificata
D69.8Other specified haemorrhagic conditions
Latin: Status haemorrhagici specificati, alii
Capillary fragility (hereditary)
Vascular pseudohaemophilia
D69.9Haemorrhagic condition, unspecified
Latin: Status haemorrhagicus, non specificatus