Chapter III
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
(D50-D89)
Certain disorders involving the immune mechanism
(D80-D89)
Includes:
* defects in the complement system
* immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
* sarcoidosis
Excludes:
* autoimmune disease (systemic) NOS (M35.9)
* functional disorders of polymorphonuclear neutrophils (D71)
* human immunodeficiency virus [HIV] disease (B20-B24)
D80 | Immunodeficiency with predominantly antibody defects Latin: Immunodeficientia cum defectibus anricorporum praedominantibus | |||||||
D80.0 | Hereditary hypogammaglobulinaemia | |||||||
Autosomal recessive agammaglobulinaemia (Swiss type) X-linked agammaglobulinaemia [Bruton] (with growth hormone deficiency) | ||||||||
D80.1 | Nonfamilial hypogammaglobulinaemia | |||||||
Agammaglobulinaemia with immunoglobulin-bearing B-lymphocytes Common variable agammaglobulinaemia [CVAgamma] Hypogammaglobulinaemia NOS | ||||||||
D80.2 | Selective deficiency of immunoglobulin A [IgA] | |||||||
D80.3 | Selective deficiency of immunoglobulin G [IgG] subclasses | |||||||
D80.4 | Selective deficiency of immunoglobulin M [IgM] | |||||||
D80.5 | Immunodeficiency with increased immunoglobulin M [IgM] | |||||||
D80.6 | Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinaemia | |||||||
D80.7 | Transient hypogammaglobulinaemia of infancy | |||||||
D80.8 | Other immunodeficiencies with predominantly antibody defects | |||||||
Kappa light chain deficiency | ||||||||
D80.9 | Immunodeficiency with predominantly antibody defects, unspecified |
D81 | Combined immunodeficiencies Latin: Immunodeficientiae combinatae | |||||||
Excludes: | autosomal recessive agammaglobulinaemia (Swiss type) (D80.0) | |||||||
D81.0 | Severe combined immunodeficiency [SCID] with reticular dysgenesis | |||||||
D81.1 | Severe combined immunodeficiency [SCID] with low T- and B-cell numbers | |||||||
D81.2 | Severe combined immunodeficiency [SCID] with low or normal B-cell numbers | |||||||
D81.3 | Adenosine deaminase [ADA] deficiency | |||||||
D81.4 | Nezelof's syndrome | |||||||
D81.5 | Purine nucleoside phosphorylase [PNP] deficiency | |||||||
D81.6 | Major histocompatibility complex class I deficiency | |||||||
Bare lymphocyte syndrome | ||||||||
D81.7 | Major histocompatibility complex class II deficiency | |||||||
D81.8 | Other combined immunodeficiencies | |||||||
Biotin-dependent carboxylase deficiency | ||||||||
D81.9 | Combined immunodeficiency, unspecified | |||||||
Severe combined immunodeficiency disorder [SCID] NOS |
D82 | Immunodeficiency associated with other major defects Latin: Immunodeficientia cum defectibus majoribus aliis associata | |||||||
Excludes: | ataxia telangiectasia [Louis-Bar] (G11.3) | |||||||
D82.0 | Wiskott-Aldrich syndrome | |||||||
Immunodeficiency with thrombocytopenia and eczema | ||||||||
D82.1 | Di George's syndrome | |||||||
Pharyngeal pouch syndrome Thymic: · alymphoplasia · aplasia or hypoplasia with immunodeficiency | ||||||||
D82.2 | Immunodeficiency with short-limbed stature | |||||||
D82.3 | Immunodeficiency following hereditary defective response to Epstein-Barr virus | |||||||
X-linked lymphoproliferative disease | ||||||||
D82.4 | Hyperimmunoglobulin E [IgE] syndrome | |||||||
D82.8 | Immunodeficiency associated with other specified major defects | |||||||
D82.9 | Immunodeficiency associated with major defect, unspecified |
D83 | Common variable immunodeficiency Latin: Immunodeficientia variabilis communis | |||||||
D83.0 | Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function | |||||||
D83.1 | Common variable immunodeficiency with predominant immunoregulatory T-cell disorders | |||||||
D83.2 | Common variable immunodeficiency with autoantibodies to B- or T-cells | |||||||
D83.8 | Other common variable immunodeficiencies | |||||||
D83.9 | Common variable immunodeficiency, unspecified |
D84 | Other immunodeficiencies Latin: Immunodeficientiae aliae | |||||||
D84.0 | Lymphocyte function antigen-1 [LFA-1] defect | |||||||
D84.1 | Defects in the complement system | |||||||
C1 esterase inhibitor [C1-INH] deficiency | ||||||||
D84.8 | Other specified immunodeficiencies | |||||||
D84.9 | Immunodeficiency, unspecified |
D86 | Sarcoidosis Latin: Sarcoidosis | |||||||
D86.0 | Sarcoidosis of lung | |||||||
D86.1 | Sarcoidosis of lymph nodes | |||||||
D86.2 | Sarcoidosis of lung with sarcoidosis of lymph nodes | |||||||
D86.3 | Sarcoidosis of skin | |||||||
D86.8 | Sarcoidosis of other and combined sites | |||||||
Iridocyclitis in sarcoidosis+ (H22.1*) Multiple cranial nerve palsies in sarcoidosis+ (G53.2*) Sarcoid: · arthropathy+ (M14.8*) · myocarditis+ (I41.8*) · myositis+ (M63.3*) Uveoparotid fever [Heerfordt] | ||||||||
D86.9 | Sarcoidosis, unspecified |
D89 | Other disorders involving the immune mechanism, not elsewhere classified Latin: Disordines immunitatis alii | |||||||
Excludes: | hyperglobulinaemia NOS (R77.1) monoclonal gammopathy (D47.2) transplant failure and rejection (T86.-) | |||||||
D89.0 | Polyclonal hypergammaglobulinaemia | |||||||
Benign hypergammaglobulinaemic purpura Polyclonal gammopathy NOS | ||||||||
D89.1 | Cryoglobulinaemia | |||||||
Cryoglobulinaemia: · essential · idiopathic · mixed · primary · secondary Cryoglobulinaemic: · purpura · vasculitis | ||||||||
D89.2 | Hypergammaglobulinaemia, unspecified | |||||||
D89.8 | Other specified disorders involving the immune mechanism, not elsewhere classified | |||||||
D89.9 | Disorder involving the immune mechanism, unspecified | |||||||
Immune disease NOS |
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