A00-B99 C00-D48D50-D89 E00-E90 F00-F99 G00-G99 H00-H59 H60-H95 I00-I99 J00-J99 K00-K93
L00-L99 M00-M99 N00-N99 O00-O99 P00-P96 Q00-Q99 R00-R99 S00-T98 V01-Y98 Z00-Z99 U00-U99

D80-D89 Certain disorders involving the immune mechanism

Chapter III

Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

Certain disorders involving the immune mechanism

* defects in the complement system
* immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
* sarcoidosis

* autoimmune disease (systemic) NOS (M35.9)
* functional disorders of polymorphonuclear neutrophils (D71)
* human immunodeficiency virus [HIV] disease (B20-B24)

D80Immunodeficiency with predominantly antibody defects
Latin: Immunodeficientia cum defectibus anricorporum praedominantibus
D80.0Hereditary hypogammaglobulinaemia
Autosomal recessive agammaglobulinaemia (Swiss type)
X-linked agammaglobulinaemia [Bruton] (with growth hormone deficiency)
D80.1Nonfamilial hypogammaglobulinaemia
Agammaglobulinaemia with immunoglobulin-bearing B-lymphocytes
Common variable agammaglobulinaemia [CVAgamma]
Hypogammaglobulinaemia NOS
D80.2Selective deficiency of immunoglobulin A [IgA]
D80.3Selective deficiency of immunoglobulin G [IgG] subclasses
D80.4Selective deficiency of immunoglobulin M [IgM]
D80.5Immunodeficiency with increased immunoglobulin M [IgM]
D80.6Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinaemia
D80.7Transient hypogammaglobulinaemia of infancy
D80.8Other immunodeficiencies with predominantly antibody defects
Kappa light chain deficiency
D80.9Immunodeficiency with predominantly antibody defects, unspecified

D81Combined immunodeficiencies
Latin: Immunodeficientiae combinatae
Excludes:autosomal recessive agammaglobulinaemia (Swiss type) (D80.0)
D81.0Severe combined immunodeficiency [SCID] with reticular dysgenesis
D81.1Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
D81.2Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
D81.3Adenosine deaminase [ADA] deficiency
D81.4Nezelof's syndrome
D81.5Purine nucleoside phosphorylase [PNP] deficiency
D81.6Major histocompatibility complex class I deficiency
Bare lymphocyte syndrome
D81.7Major histocompatibility complex class II deficiency
D81.8Other combined immunodeficiencies
Biotin-dependent carboxylase deficiency
D81.9Combined immunodeficiency, unspecified
Severe combined immunodeficiency disorder [SCID] NOS

D82Immunodeficiency associated with other major defects
Latin: Immunodeficientia cum defectibus majoribus aliis associata
Excludes:ataxia telangiectasia [Louis-Bar] (G11.3)
D82.0Wiskott-Aldrich syndrome
Immunodeficiency with thrombocytopenia and eczema
D82.1Di George's syndrome
Pharyngeal pouch syndrome
· alymphoplasia
· aplasia or hypoplasia with immunodeficiency
D82.2Immunodeficiency with short-limbed stature
D82.3Immunodeficiency following hereditary defective response to Epstein-Barr virus
X-linked lymphoproliferative disease
D82.4Hyperimmunoglobulin E [IgE] syndrome
D82.8Immunodeficiency associated with other specified major defects
D82.9Immunodeficiency associated with major defect, unspecified

D83Common variable immunodeficiency
Latin: Immunodeficientia variabilis communis
D83.0Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function
D83.1Common variable immunodeficiency with predominant immunoregulatory T-cell disorders
D83.2Common variable immunodeficiency with autoantibodies to B- or T-cells
D83.8Other common variable immunodeficiencies
D83.9Common variable immunodeficiency, unspecified

D84Other immunodeficiencies
Latin: Immunodeficientiae aliae
D84.0Lymphocyte function antigen-1 [LFA-1] defect
D84.1Defects in the complement system
C1 esterase inhibitor [C1-INH] deficiency
D84.8Other specified immunodeficiencies
D84.9Immunodeficiency, unspecified

Latin: Sarcoidosis
D86.0Sarcoidosis of lung
D86.1Sarcoidosis of lymph nodes
D86.2Sarcoidosis of lung with sarcoidosis of lymph nodes
D86.3Sarcoidosis of skin
D86.8Sarcoidosis of other and combined sites
Iridocyclitis in sarcoidosis+ (H22.1*)
Multiple cranial nerve palsies in sarcoidosis+ (G53.2*)
· arthropathy+ (M14.8*)
· myocarditis+ (I41.8*)
· myositis+ (M63.3*)
Uveoparotid fever [Heerfordt]
D86.9Sarcoidosis, unspecified

D89Other disorders involving the immune mechanism, not elsewhere classified
Latin: Disordines immunitatis alii
Excludes:hyperglobulinaemia NOS (R77.1)
monoclonal gammopathy (D47.2)
transplant failure and rejection (T86.-)
D89.0Polyclonal hypergammaglobulinaemia
Benign hypergammaglobulinaemic purpura
Polyclonal gammopathy NOS
· essential
· idiopathic
· mixed
· primary
· secondary
· purpura
· vasculitis
D89.2Hypergammaglobulinaemia, unspecified
D89.8Other specified disorders involving the immune mechanism, not elsewhere classified
D89.9Disorder involving the immune mechanism, unspecified
Immune disease NOS