A00-B99 C00-D48D50-D89 E00-E90 F00-F99 G00-G99 H00-H59 H60-H95 I00-I99 J00-J99 K00-K93
L00-L99 M00-M99 N00-N99 O00-O99 P00-P96 Q00-Q99 R00-R99 S00-T98 V01-Y98 Z00-Z99 U00-U99

G10-G13 Systemic atrophies primarily affecting the central nervous system




 
Chapter VI

Diseases of the nervous system
(G00-G99)

Systemic atrophies primarily affecting the central nervous system
(G10-G13)

G10Huntington's disease
Latin: Morbus Huntington
Huntington's chorea

G11Hereditary ataxia
Latin: Ataxia hereditaria
Excludes:cerebral palsy (G80.-)
hereditary and idiopathic neuropathy (G60.-)
metabolic disorders (E70-E90)
G11.0Congenital nonprogressive ataxia
Latin: Ataxia non progressiva congenita
G11.1Early-onset cerebellar ataxia
Latin: Ataxia cerebellaris juvenili
Note:Onset usually before the age of 20
Early-onset cerebellar ataxia with:
· essential tremor
· myoclonus [Hunt's ataxia]
· retained tendon reflexes
Friedreich's ataxia (autosomal recessive)
X-linked recessive spinocerebellar ataxia
G11.2Late-onset cerebellar ataxia
Latin: Ataxia cerebellaris tardiva
Note:Onset usually after the age of 20
G11.3Cerebellar ataxia with defective DNA repair
Latin: Ataxia cerebellaris cum detectu DNA
Ataxia telangiectasia [Louis-Bar]
Excludes:Cockayne's syndrome (Q87.1)
xeroderma pigmentosum (Q82.1)
G11.4Hereditary spastic paraplegia
Latin: Paraplegia spastica hereditaria
G11.8Other hereditary ataxias
Latin: Ataxiae hereditariae aliae
G11.9Hereditary ataxia, unspecified
Latin: Ataxia hereditaria, non specificata
Hereditary cerebellar:
· ataxia NOS
· degeneration
· disease
· syndrome

G12Spinal muscular atrophy and related syndromes
Latin: Atrophia musculorum spinalis et syndromae affines
G12.0Infantile spinal muscular atrophy, type I [Werdnig-Hoffman]
Latin: Atrophia musculorum spinalis infantilis, typus I (Werding-Hoffman)
G12.1Other inherited spinal muscular atrophy
Latin: Atrophia musculorum spinalis hereditaria alia
Progressive bulbar palsy of childhood [Fazio-Londe]
Spinal muscular atrophy:
· adult form
· childhood form, type II
· distal
· juvenile form, type III [Kugelberg-Welander]
· scapuloperoneal form
G12.2Motor neuron disease
Latin: Morbus neuroni motorii
Familial motor neuron disease
Lateral sclerosis:
· amyotrophic
· primary
Progressive:
· bulbar palsy
· spinal muscular atrophy
G12.8Other spinal muscular atrophies and related syndromes
Latin: Atrophiae musculorum spinales aliae et syndromae affines
G12.9Spinal muscular atrophy, unspecified
Latin: Atrophia musculorum spinalis, non specificata

G13*Systemic atrophies primarily affecting central nervous system in diseases classified elsewhere
Latin: Atrophiae systematis nervosi centralis in morbis aliis
G13.0*Paraneoplastic neuromyopathy and neuropathy
Latin: Neuropathia et neuromyopathia paraneoplastica
Carcinomatous neuromyopathy (C00-C97+)
Sensorial paraneoplastic neuropathy [Denny Brown] (C00-D48+)
G13.1*Other systemic atrophy primarily affecting central nervous system in neoplastic disease
Latin: Atrophia systematis nervosi centralis neoplastica alia
Paraneoplastic limbic encephalopathy (C00-D48+)
G13.2*Systemic atrophy primarily affecting central nervous system in myxoedema (E00.1+, E03.-+)
Latin: Atrophia systematis nervosi centralis ad cretenismum (E00.1+, E03.-+)
G13.8*Systemic atrophy primarily affecting central nervous system in other diseases classified elsewhere
Latin: Atrophia systematis nervosi centralis in morbis aliis