A00-B99 C00-D48D50-D89 E00-E90 F00-F99 G00-G99 H00-H59 H60-H95 I00-I99 J00-J99 K00-K93
L00-L99 M00-M99 N00-N99 O00-O99 P00-P96 Q00-Q99 R00-R99 S00-T98 V01-Y98 Z00-Z99 U00-U99

I30-I52 Other forms of heart disease




 
Chapter IX

Diseases of the circulatory system
(I00-I99)

Other forms of heart disease
(I30-I52)

I30Acute pericarditis
Latin: Pericarditis acuta
Includes:acute pericardial effusion
Excludes:rheumatic pericarditis (acute) (I01.0)
I30.0Acute nonspecific idiopathic pericarditis
Latin: Pericarditis idopathica acuta, non specificata
I30.1Infective pericarditis
Latin: Pericarditis infectiva
Pericarditis:
· pneumococcal
· purulent
· staphylococcal
· streptococcal
· viral
Pyopericarditis
Use additional code (B95-B97), if desired, to identify infectious agent.
I30.8Other forms of acute pericarditis
Latin: Pericarditis acuta, formae aliae
I30.9Acute pericarditis, unspecified
Latin: Pericarditis acuta, non specificata

I31Other diseases of pericardium
Latin: Morbi pericardii alii
Excludes:current complications following acute myocardial infarction (I23.-)
postcardiotomy syndrome (I97.0)
trauma (S26.-)
when specified as rheumatic (I09.2)
I31.0Chronic adhesive pericarditis
Latin: Pericarditis adhaesiva chronica
Accretio cordis
Adherent pericardium
Adhesive mediastinopericarditis
I31.1Chronic constrictive pericarditis
Latin: Pericarditis constrictiva chronica
Concretio cordis
Pericardial calcification
I31.2Haemopericardium, not elsewhere classified
Latin: Haemopericardium
I31.3Pericardial effusion (noninflammatory)
Latin: Exsudatio pericardii non inflammatoria
Chylopericardium
I31.8Other specified diseases of pericardium
Latin: Morbi pericardii specificati, alii
Epicardial plaques
Focal pericardial adhesions
I31.9Disease of pericardium, unspecified
Latin: Morbus pericardii, non specificatus
Cardiac tamponade
Pericarditis (chronic) NOS

I32*Pericarditis in diseases classified elsewhere
Latin: Pericarditis in morbis aliis
I32.0*Pericarditis in bacterial diseases classified elsewhere
Latin: Pericarditis in morbis bacterialibus aliis
Pericarditis:
· gonococcal (A54.8+)
· meningococcal (A39.5+)
· syphilitic (A52.0+)
· tuberculous (A18.8+)
I32.1*Pericarditis in other infectious and parasitic diseases classified elsewhere
Latin: Pericarditis in morbis infectivis et morbis parasitariis
I32.8*Pericarditis in other diseases classified elsewhere
Latin: Pericarditides aliae in morbis aliis
Pericarditis (in):
· rheumatoid (M05.3+)
· systemic lupus erythematosus (M32.1+)
· uraemic (N18.8+)

I33Acute and subacute endocarditis
Latin: Endocarditis acuta et endocarditis subacuta
Excludes:acute rheumatic endocarditis (I01.1)
endocarditis NOS (I38)
I33.0Acute and subacute infective endocarditis
Latin: Endocarditis infectiva acuta et endocarditis subacuta
Endocarditis (acute)(subacute):
·bacterial
· infective NOS
· lenta
· malignant
· septic
· ulcerative
Use additional code (B95-B97), if desired, to identify infectious agent.
I33.9Acute endocarditis, unspecified
Latin: Endocarditis acuta, non specificata
Endocarditis
Myoendocarditis
Periendocarditis
}
}
}
acute or subacute

I34Nonrheumatic mitral valve disorders
Latin: Morbi valvulae mitralis, non rheumatici
Excludes:mitral (valve):
· disease (I05.9)
· failure (I05.8)
· stenosis (I05.0)
when of unspecified cause but with mention of:
· diseases of aortic valve (I08.0)
· mitral stenosis or obstruction (I05.0)
when specified as congenital (Q23.2, Q23.3)
when specified as rheumatic (I05.-)
I34.0Mitral (valve) insufficiency
Latin: Insufficientia valvulae mitralis non rheumatica
Mitral (valve):
· incompetence
· regurgitation
}
}
NOS or of specified cause, except rheumatic
I34.1Mitral (valve) prolapse
Latin: Prolapsus valvulae mitralis
Floppy mitral valve syndrome
Excludes:Marfan's syndrome (Q87.4)
I34.2Nonrheumatic mitral (valve) stenosis
Latin: Stenosis valvulae mitralis non rheumatica
I34.8Other nonrheumatic mitral valve disorders
Latin: Morbi valvulae mitralis non rheumatici alii
I34.9Nonrheumatic mitral valve disorder, unspecified
Latin: Morbus valvulae mitralis non rheumaticus, non specificatus

I35Nonrheumatic aortic valve disorders
Latin: Morbi valvulae aortae non rheumatici
Excludes:hypertrophic subaortic stenosis (I42.1)
when of unspecified cause but with mention of diseases of mitral valve (I08.0)
when specified as congenital (Q23.0, Q23.1)
when specified as rheumatic (I06.-)
I35.0Aortic (valve) stenosis
Latin: Stenosis valvulae aortae non rheumatica
I35.1Aortic (valve) insufficiency
Latin: Insufficientia valvularum aortae non rheumatica
Aortic (valve):
· incompetence
· regurgitation
}
}
NOS or of specified cause, except rheumatic
I35.2Aortic (valve) stenosis with insufficiency
Latin: Stenosis cum insufficientia valvulae aortae, non rheumatica
I35.8Other aortic valve disorders
Latin: Morbi valvulae aortae non rheumatici alii
I35.9Aortic valve disorder, unspecified
Latin: Morbus valvulae aortae non rheumaticus, non specificatus

I36Nonrheumatic tricuspid valve disorders
Latin: Morbi valvulae tricuspidalis non rheumatici
Excludes:when of unspecified cause (I07.-)
when specified as congenital (Q22.4, Q22.8, Q22.9)
when specified as rheumatic (I07.-)
I36.0Nonrheumatic tricuspid (valve) stenosis
Latin: Stenosis valvulae tricuspidalis non rheumatica
I36.1Nonrheumatic tricuspid (valve) insufficiency
Latin: Insufficientia valvulae tricuspidalis non rheumatica
Tricuspid (valve):
· incompetence
· regurgitation
}
}
of specified cause, except rheumatic
I36.2Nonrheumatic tricuspid (valve) stenosis with insufficiency
Latin: Stenosis cum insufficientia valvulae tricuspidalis non rheumatica
I36.8Other nonrheumatic tricuspid valve disorders
Latin: Morbi valvulae tricuspidalis non rheumatici alii
I36.9Nonrheumatic tricuspid valve disorder, unspecified
Latin: Morbus valvulae tricuspidalis non rheumaticus, non specificatus

I37Pulmonary valve disorders
Latin: Morbi valvulae pulmonalis
Excludes:when specified as congenital (Q22.1, Q22.2, Q22.3)
when specified as rheumatic (I09.8)
I37.0Pulmonary valve stenosis
Latin: Stenosis valvulae pulmonalis
I37.1Pulmonary valve insufficiency
Latin: Insufficientia valvulae pulmonalis
Pulmonary valve:
· incompetence
· regurgitation
}
}
NOS or of specified cause, except rheumatic
I37.2Pulmonary valve stenosis with insufficiency
Latin: Stenosis cum insufficientia valvulae pulmonalis
I37.8Other pulmonary valve disorders
Latin: Morbi valvulae pulmonalis alii
I37.9Pulmonary valve disorder, unspecified
Latin: Morbus valvulae pulmonalis, non specificatus

I38Endocarditis, valve unspecified
Latin: Endocarditis valvulae, non specificata
Endocarditis (chronic) NOS
Valvular:
· incompetence
· insufficiency
· regurgitation
· stenosis
Valvulitis (chronic)
}
}
}
}
}
}
of unspecified valve
{
{
NOS or of specified cause, except rheumatic or congenital
Excludes:congenital insufficiency of cardiac valve NOS (Q24.8)
congenital stenosis of cardiac valve NOS (Q24.8)
endocardial fibroelastosis (I42.4)
when specified as rheumatic (I09.1)

I39*Endocarditis and heart valve disorders in diseases classified elsewhere
Latin: Endocarditis et morbi valvulae cordis in morbis aliis
Includes:endocardial involvement in:
· candidal infection (B37.6+)
· gonococcal infection (A54.8+)
· Libman-Sacks disease (M32.1+)
· meningococcal infection (A39.5+)
· rheumatoid arthritis (M05.3+)
· syphilis (A52.0+)
· tuberculosis (A18.8+)
· typhoid fever (A01.0+)
I39.0*Mitral valve disorders in diseases classified elsewhere
Latin: Morbi valvulae mitralis in morbis aliis
I39.1*Aortic valve disorders in diseases classified elsewhere
Latin: Morbi valvulae aortae in morbis aliis
I39.2*Tricuspid valve disorders in diseases classified elsewhere
Latin: Morbi valvulae tricuspidalis in morbis aliis
I39.3*Pulmonary valve disorders in diseases classified elsewhere
Latin: Morbi valvulae pulmonalis in morbis aliis
I39.4*Multiple valve disorders in diseases classified elsewhere
Latin: Morbi valvularum multiplicium in morbis aliis
I39.8*Endocarditis, valve unspecified, in diseases classified elsewhere
Latin: Endocarditis valvulae non specificatae in morbis aliis

I40Acute myocarditis
Latin: Myocarditis acuta
I40.0Infective myocarditis
Latin: Myocarditis infectiva
Septic myocarditis
Use additional code (B95-B97), if desired, to identify infectious agent.
I40.1Isolated myocarditis
Latin: Myocarditis monosymptomatica
I40.8Other acute myocarditis
Latin: Myocarditis acuta alia
I40.9Acute myocarditis, unspecified
Latin: Myocarditis acuta,non specificata

I41*Myocarditis in diseases classified elsewhere
Latin: Myocarditis in morbis aliis
I41.0*Myocarditis in bacterial diseases classified elsewhere
Latin: Myocarditis in morbis bacterialibus
Myocarditis:
· diphtheritic (A36.8+)
· gonococcal (A54.8+)
· meningococcal (A39.5+)
· syphilitic (A52.0+)
· tuberculous (A18.8+)
I41.1*Myocarditis in viral diseases classified elsewhere
Latin: Myocarditis in morbis viralibus
Influenzal myocarditis (acute):
· avian influenza virus identified (J09+)
· other virus identified (J10.8+)
· virus not identified (J11.8+)
Mumps myocarditis (B26.8+)
I41.2*Myocarditis in other infectious and parasitic diseases classified elsewhere
Latin: Myocarditis in morbis infectivis et morbis parasitariis
Myocarditis in:
· Chagas' disease (chronic) (B57.2+)
· acute (B57.0+)
· toxoplasmosis (B58.8+)
I41.8*Myocarditis in other diseases classified elsewhere
Latin: Myocarditis in morbis aliis
Rheumatoid myocarditis (M05.3+)
Sarcoid myocarditis (D86.8+)

I42Cardiomyopathy
Latin: Cardiomyopathia
Excludes:cardiomyopathy complicating:
· pregnancy (O99.4)
· puerperium (O90.3)
ischaemic cardiomyopathy (I25.5)
I42.0Dilated cardiomyopathy
Latin: Cardiomyopathia congestiva
Congestive cardiomyopathy
I42.1Obstructive hypertrophic cardiomyopathy
Latin: Cardiomyopathia hypertrophica obstructiva
Hypertrophic subaortic stenosis
I42.2Other hypertrophic cardiomyopathy
Latin: Cardiomyopathia hypertrophica alia
Nonobstructive hypertrophic cardiomyopathy
I42.3Endomyocardial (eosinophilic) disease
Latin: Endomyocarditis eosinophilica
Endomyocardial (tropical) fibrosis
Löffler's endocarditis
I42.4Endocardial fibroelastosis
Latin: Fibroelastosis endocardii
Congenital cardiomyopathy
I42.5Other restrictive cardiomyopathy
Latin: Cardiomyopathia restrictiva alia
Constrictive cardiomyopathy NOS
I42.6Alcoholic cardiomyopathy
Latin: Cardiomyopathia alcoholica
I42.7Cardiomyopathy due to drugs and other external agents
Latin: Cardiomyopathia propter usum medicamentorum et factores externo alios
Use additional external cause code (Chapter XX), if desired, to identify cause.
I42.8Other cardiomyopathies
Latin: Cardiomyopathiae aliae
I42.9Cardiomyopathy, unspecified
Latin: Cardiomyopathia, non specificata
Cardiomyopathy (primary)(secondary) NOS

I43*Cardiomyopathy in diseases classified elsewhere
Latin: Cardiomyopathia in morbis aliis
I43.0*Cardiomyopathy in infectious and parasitic diseases classified elsewhere
Latin: Cardiomyopathia in morbis infectivis et morbis parasitariis
Cardiomyopathy in diphtheria (A36.8+)
I43.1*Cardiomyopathy in metabolic diseases
Latin: Cardiomyopathia in morbis metabolicis
Cardiac amyloidosis (E85.-+)
I43.2*Cardiomyopathy in nutritional diseases
Latin: Cardiomyopathia in morbis nutritionalibus
Nutritional cardiomyopathy NOS (E63.9+)
I43.8*Cardiomyopathy in other diseases classified elsewhere
Latin: Cardiomyopathiae in morbis aliis
Gouty tophi of heart (M10.0+)
Thyrotoxic heart disease (E05.9+)

I44Atrioventricular and left bundle-branch block
Latin: Block atrioventricularis et block rami sinistri
I44.0Atrioventricular block, first degree
Latin: Block atrioventricularis, gradus primus
I44.1Atrioventricular block, second degree
Latin: Block atrioventricularis, gradus secundus
Atrioventricular block, type I and II
Möbitz block, type I and II
Second-degree block, type I and II
Wenckebach's block
I44.2Atrioventricular block, complete
Latin: Block atrioventricularis completus (totalis)
Complete heart block NOS
Third-degree block
I44.3Other and unspecified atrioventricular block
Latin: Block atrioventricularis allus et non specificatus
Atrioventricular block NOS
I44.4Left anterior fascicular block
Latin: Block fasciculi anterioris, rami atrioventricularis sinistri
I44.5Left posterior fascicular block
Latin: Block fasciculi posterioris, rami atrioventricularis sinistri
I44.6Other and unspecified fascicular block
Latin: Block fasciculi alterius et non specificati
Left bundle-branch hemiblock NOS
I44.7Left bundle-branch block, unspecified
Latin: Block fasciculi sinistri, non specificatus

I45Other conduction disorders
Latin: Disordines systematis conductivi cordis alii
I45.0Right fascicular block
Latin: Block fasciculi dextri
I45.1Other and unspecified right bundle-branch block
Latin: Block fasciculi dextri alius et non specificatus
Right bundle-branch block NOS
I45.2Bifascicular block
Latin: Block bifascicularis
I45.3Trifascicular block
Latin: Block trifascicularis
I45.4Nonspecific intraventricular block
Latin: Block intraventricularis, non specificatus
Bundle-branch block NOS
I45.5Other specified heart block
Latin: Block cordis specificatus, alius
Sinoatrial block
Sinoauricular block
Excludes:heart block NOS (I45.9)
I45.6Pre-excitation syndrome
Latin: Syndroma praeexcitationis
Anomalous atrioventricular excitation
Atrioventricular conduction:
· accelerated
· accessory
· pre-excitation
Lown-Ganong-Levine syndrome
Wolff-Parkinson-White syndrome
I45.8Other specified conduction disorders
Latin: Disordines systematis conductivi cordis specificati alii
Atrioventricular [AV] dissociation
Interference dissociation
I45.9Conduction disorder, unspecified
Latin: Disordo conductionis, non specificatus
Heart block NOS
Stokes-Adams syndrome

I46Cardiac arrest
Latin: Institio cordis
Excludes:cardiogenic shock (R57.0)
complicating:
· abortion or ectopic or molar pregnancy (O00-O07, O08.8)
· obstetric surgery and procedures (O75.4)
I46.0Cardiac arrest with successful resuscitation
Latin: Institio cordis cum reanimatione positiva
I46.1Sudden cardiac death, so described
Latin: Mors cardiaca subita
Excludes:sudden death:
· NOS (R96.-)
· with:
  · conduction disorder (I44-I45)
  · myocardial infarction (I21-I22)
I46.9Cardiac arrest, unspecified
Latin: Institio cordis, non specificata

I47Paroxysmal tachycardia
Latin: Tachycardia paraoxysmalis
Excludes:complicating:
· abortion or ectopic or molar pregnancy (O00-O07, O08.8)
· obstetric surgery and procedures (O75.4)
tachycardia:
· NOS (R00.0)
· sinoauricular NOS (R00.0)
· sinus [sinusal] NOS (R00.0)
I47.0Re-entry ventricular arrhythmia
Latin: Arrhytmia ventricularis paroxysmalis
I47.1Supraventricular tachycardia
Latin: Tachycardia supraventricularis
Paroxysmal tachycardia:
· atrial
· atrioventricular [AV]
· junctional
· nodal
I47.2Ventricular tachycardia
Latin: Tachycardia ventricularis paroxysmalis
I47.9Paroxysmal tachycardia, unspecified
Latin: Tachycardia paroxysmalis, non specificata
Bouveret(-Hoffmann) syndrome

I48Atrial fibrillation and flutter
Latin: Fibrillatio atriorum et fluctuatio atriorum

I49Other cardiac arrhythmias
Latin: Arrhytmiae cordis aliae
Excludes:bradycardia:
· NOS (R00.1)
· sinoatrial (R00.1)
· sinus (R00.1)
· vagal (R00.1)
complicating:
· abortion or ectopic or molar pregnancy (O00-O07, O08.8)
· obstetric surgery and procedures (O75.4)
neonatal cardiac dysrhythmia (P29.1)
I49.0Ventricular fibrillation and flutter
Latin: Fibrillatio ventriculorum et fluctuatio ventriculorum
I49.1Atrial premature depolarization
Latin: Extrasystole supraventricularis
Atrial premature beats
I49.2Junctional premature depolarization
Latin: Extrasystole nodalis
I49.3Ventricular premature depolarization
Latin: Extrasystole ventricularis
I49.4Other and unspecified premature depolarization
Latin: Extrasystole alia, non specificata
Ectopic beats
Extrasystoles
Extrasystolic arrhythmias
Premature:
· beats NOS
· contractions
I49.5Sick sinus syndrome
Latin: Disordo sinus cordi
Tachycardia-bradycardia syndrome
I49.8Other specified cardiac arrhythmias
Latin: Arrhytmiae cordis specificatae, aliae
Rhythm disorder:
· coronary sinus
· ectopic
· nodal
I49.9Cardiac arrhythmia, unspecified
Latin: Arrhytmia cordis, non specificata
Arrhythmia (cardiac) NOS

I50Heart failure
Latin: Insufficientia cordis
Excludes:complicating:
· abortion or ectopic or molar pregnancy (O00-O07, O08.8)
· obstetric surgery and procedures (O75.4)
due to hypertension (I11.0)
· with renal disease (I13.-)
following cardiac surgery or due to presence of cardiac prosthesis (I97.1)
neonatal cardiac failure (P29.0)
I50.0Congestive heart failure
Latin: Insufficientia cordis congestiva
Congestive heart disease
Right ventricular failure (secondary to left heart failure)
I50.1Left ventricular failure
Latin: Insufficientia ventriculi sinistri
Cardiac asthma
Left heart failure
Oedema of lung
Pulmonary oedema
}
}
with mention of heart disease NOS or heart failure
I50.9Heart failure, unspecified
Latin: Insufficientia cordis, non specificata
Cardiac, heart or myocardial failure NOS

I51Complications and ill-defined descriptions of heart disease
Latin: Complicationes et morbi cordis male definiti
Excludes:any condition in I51.4-I51.9 due to hypertension (I11.-)
· with renal disease (I13.-)
complications following acute myocardial infarction (I23.-)
when specified as rheumatic (I00-I09)
I51.0Cardiac septal defect, acquired
Latin: Complicationes et morbi cordis male definiti
Acquired septal defect (old):
· atrial
· auricular
· ventricular
I51.1Rupture of chordae tendineae, not elsewhere classified
Latin: Ruptura chordae tendineae cordis
I51.2Rupture of papillary muscle, not elsewhere classified
Latin: Ruptura muscull papillaris cordis
I51.3Intracardiac thrombosis, not elsewhere classified
Latin: Thrombosis intaracardiaca
Thrombosis (old):
· apical
· atrial
· auricular
· ventricular
I51.4Myocarditis, unspecified
Latin: Myocarditis, non specificata
Myocardial fibrosis
Myocarditis:
· NOS
· chronic (interstitial)
I51.5Myocardial degeneration
Latin: Degeneratio myocardii
Degeneration of heart or myocardium:
· fatty
· senile
Myocardial disease
I51.6Cardiovascular disease, unspecified
Latin: Morbus cardiovascularis, non specificatus
Cardiovascular accident NOS
Excludes:atherosclerotic cardiovascular disease, so described (I25.0)
I51.7Cardiomegaly
Latin: Cardiomegalia
Cardiac:
· dilatation
· hypertrophy
Ventricular dilatation
I51.8Other ill-defined heart diseases
Latin: Morbis cordis alli
Carditis (acute)(chronic)
Pancarditis (acute)(chronic)
I51.9Heart disease, unspecified
Latin: Morbus cordis, non specificatus

I52*Other heart disorders in diseases classified elsewhere
Latin: Morbi cordis alii in morbis aliis
Excludes:cardiovascular disorders NOS in diseases classified elsewhere (I98.-*)
I52.0*Other heart disorders in bacterial diseases classified elsewhere
Latin: Morbi cordis alii in morbis bacterialibus
Meningococcal carditis NEC (A39.5+)
I52.1*Other heart disorders in other infectious and parasitic diseases classified elsewhere
Latin: Morbi cordis alii in morbis infectivis et morbis parasitariis
Pulmonary heart disease in schistosomiasis (B65.-+)
I52.8*Other heart disorders in other diseases classified elsewhere
Latin: Morbi cordis alii in morbis aliis
Rheumatoid carditis (M05.3+)


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