Chapter XII
Diseases of the skin and subcutaneous tissue
(L00-L99)
Bullous disorders
(L10-L14)
Excludes:
* benign familial pemphigus [Hailey-Hailey] (Q82.8)
* staphylococcal scalded skin syndrome (L00)
* toxic epidermal necrolysis [Lyell] (L51.2)
L10 | Pemphigus Latin: Pemphigus | |||||||
Excludes: | pemphigus neonatorum (L00) | |||||||
L10.0 | Pemphigus vulgaris Latin: Pemphigus vulgaris | |||||||
L10.1 | Pemphigus vegetans Latin: Pemphigus vegetans | |||||||
L10.2 | Pemphigus foliaceus Latin: Pemphigus foliaceus | |||||||
L10.3 | Brazilian pemphigus [fogo selvagem] Latin: Pemphigus brazilicus | |||||||
L10.4 | Pemphigus erythematosus Latin: Pemphigus erythematosus | |||||||
Senear-Usher syndrome | ||||||||
L10.5 | Drug-induced pemphigus Latin: Pemphigus medicamentosus | |||||||
Use additional external cause code (Chapter XX), if desired, to identify drug. | ||||||||
L10.8 | Other pemphigus Latin: Pemphigus alius | |||||||
L10.9 | Pemphigus, unspecified Latin: Pemphigus, non specificatus |
L11 | Other acantholytic disorders Latin: Acantholysis alia | |||||||
L11.0 | Acquired keratosis follicularis Latin: Keratosis follicularis acquisita | |||||||
Excludes: | keratosis follicularis (congenital) [Darier-White] (Q82.8) | |||||||
L11.1 | Transient acantholytic dermatosis [Grover] Latin: Dermatosis acantholytica transitiva (Grover) | |||||||
L11.8 | Other specified acantholytic disorders Latin: Acantholyses aliae, specificatae | |||||||
L11.9 | Acantholytic disorder, unspecified Latin: Acantholysis, non specificata |
L12 | Pemphigoid Latin: Pemphigoides | |||||||
Excludes: | herpes gestationis (O26.4) impetigo herpetiformis (L40.1) | |||||||
L12.0 | Bullous pemphigoid Latin: Pemphigoides bullosus | |||||||
L12.1 | Cicatricial pemphigoid Latin: Pemphigoides cicatricialis | |||||||
Benign mucous membrane pemphigoid | ||||||||
L12.2 | Chronic bullous disease of childhood Latin: Dermatitis bullosa infantilis chronica | |||||||
Juvenile dermatitis herpetiformis | ||||||||
L12.3 | Acquired epidermolysis bullosa Latin: Epidermolysis bullosa acquisita | |||||||
Excludes: | epidermolysis bullosa (congenital) (Q81.-) | |||||||
L12.8 | Other pemphigoid Latin: Pemphigoides alius | |||||||
L12.9 | Pemphigoid, unspecified Latin: Pemphigoides, non specificatus |
L13 | Other bullous disorders Latin: Dermatitis bullosa alia | |||||||
L13.0 | Dermatitis herpetiformis Latin: Dermatitis herpetiformis | |||||||
Duhring's disease | ||||||||
L13.1 | Subcorneal pustular dermatitis Latin: Dermatitis pustulosa subcornealis | |||||||
Sneddon-Wilkinson disease | ||||||||
L13.8 | Other specified bullous disorders Latin: Dermatitis bullosa alia, specificata | |||||||
L13.9 | Bullous disorder, unspecified Latin: Dermatitis bullosa, non specificata |
L14* | Bullous disorders in diseases classified elsewhere Latin: Dermatitis bullosa in morbis aliis |
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