Chapter XIII
Diseases of the musculoskeletal system and connective tissue
(M00-M99)
Systemic connective tissue disorders
(M30-M36)
Includes:
autoimmune disease:
· NOS
· systemic
collagen (vascular) disease:
· NOS
· systemic
Excludes:
autoimmune disease, single organ or single cell-type (code to relevant condition category)
M30 | Polyarteritis nodosa and related conditions Latin:Polyarteritis nodosa et morbi affines | |||||||
M30.0 | Polyarteritis nodosa Latin: Polyarteritis nodosa | |||||||
M30.1 | Polyarteritis with lung involvement [Churg-Strauss] Latin: Polyarteritis pulmonis (Churg-Strauss) | |||||||
Allergic granulomatous angiitis | ||||||||
M30.2 | Juvenile polyarteritis Latin: Polyarteritis juvenilis | |||||||
M30.3 | Mucocutaneous lymph node syndrome [Kawasaki] Latin: Syndroma nodi lymphatici mucocutanea (Kawasaki) | |||||||
M30.8 | Other conditions related to polyarteritis nodosa Latin: Status similes cum polyarteritide nodosa connexi alii | |||||||
Polyangiitis overlap syndrome |
M31 | Other necrotizing vasculopathies Latin: Vasculopathiae necroticae aliae | |||||||
M31.0 | Hypersensitivity angiitis Latin: Angiitis hypersensitiva | |||||||
Goodpasture's syndrome | ||||||||
M31.1 | Thrombotic microangiopathy Latin: Microangiopathia thrombotica | |||||||
Thrombotic thrombocytopenic purpura | ||||||||
M31.2 | Lethal midline granuloma
Latin: Granuloma centrale letale | |||||||
M31.3 | Wegener's granulomatosis Latin: Granulomatosis Wegner |
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Necrotizing respiratory granulomatosis | ||||||||
M31.4 | Aortic arch syndrome [Takayasu]
Latin: Syndroma arcus aortae (Takayasu) | |||||||
M31.5 | Giant cell arteritis with polymyalgia rheumatica Latin: Arteritis gigantocellularis cum polymyalgia rheumatica | |||||||
M31.6 | Other giant cell arteritis Latin: Arteritis gigantocellularis alia | |||||||
M31.7 | Microscopic polyangiitis Latin: . | |||||||
Microscopic polyarteritis | ||||||||
Excludes: | polyarteritis nodosa (M30.0) | |||||||
M31.8 | Other specified necrotizing vasculopathies Latin: Vasculopathiae necroticae aliae, specificatae | |||||||
Hypocomplementaemic vasculitis | ||||||||
M31.9 | Necrotizing vasculopathy, unspecified
Latin: Vasculopathia necrotica, non specificata |
M32 | Systemic lupus erythematosus Latin: Lupus erythematosus systemicus | |||||||
Excludes: | lupus erythematosus (discoid)(NOS) (L93.0) | |||||||
M32.0 | Drug-induced systemic lupus erythematosus Latin: Lupus erythematosus systematicus medicamentosus |
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Use additional external cause code (Chapter XX), if desired, to identify drug. | ||||||||
M32.1+ | Systemic lupus erythematosus with organ or system involvement Latin: Lupus erythematosus systemicus cum organo sive systemate apprehendenti | |||||||
Libman-Sacks disease (I39.-*) Lupus pericarditis (I32.8*) Systemic lupus erythematosus with: · kidney involvement (N08.5*, N16.4*) · lung involvement (J99.1*) | ||||||||
M32.8 | Other forms of systemic lupus erythematosus Latin: Lupus erythematosus systemicus, formae aliae | |||||||
M32.9 | Systemic lupus erythematosus, unspecified Latin: Lupus erythematosus systemicus, non specificatus |
M33 | Dermatopolymyositis Latin: Dermatopolymyositis | |||||||
M33.0 | Juvenile dermatomyositis Latin: Dermatomyositis puerilis | |||||||
M33.1 | Other dermatomyositis Latin: Dermatomyositis alia | |||||||
M33.2 | Polymyositis Latin: Polymyositis | |||||||
M33.9 | Dermatopolymyositis, unspecified Latin: Dermatopolymyositis, non specificata |
M34 | Systemic sclerosis Latin: Scleroderma | |||||||
Includes: | scleroderma | |||||||
Excludes: | scleroderma:
· circumscribed (L94.0) · neonatal (P83.8) | |||||||
M34.0 | Progressive systemic sclerosis Latin: Scleroderma progressivum diffusum | |||||||
M34.1 | CR(E)ST syndrome Latin: Syndroma CREST | |||||||
Combination of calcinosis, Raynaud's phenomenon, (o)esophageal dysfunction, sclerodactyly, telangiectasia. | ||||||||
M34.2 | Systemic sclerosis induced by drugs and chemicals Latin: Scleroderma medicamentosum et chemicalis | |||||||
Use additional external cause code (Chapter XX), if desired, to identify cause. | ||||||||
M34.8 | Other forms of systemic sclerosis Latin: Scleroderma, formae aliae | |||||||
Systemic sclerosis with: · lung involvement+ (J99.1*) · myopathy+ (G73.7*) | ||||||||
M34.9 | Systemic sclerosis, unspecified Latin: Scleroderma, non specificatum |
M35 | Other systemic involvement of connective tissue Latin: Morbi textus connexivi systemici alii | |||||||
Excludes: | reactive perforating collagenosis (L87.1) | |||||||
M35.0 | Sicca syndrome [Sjögren] Latin: Syndroma sicca (Sjogren) | |||||||
Sjögren's syndrome with: · keratoconjunctivitis+ (H19.3*) · lung involvement+ (J99.1*) · myopathy+ (G73.7*) · renal tubulo-interstitial disorders+ (N16.4*) | ||||||||
M35.1 | Other overlap syndromes Latin: Syndromae flectentes aliae | |||||||
Mixed connective tissue disease | ||||||||
Excludes: | polyangiitis overlap syndrome (M30.8) | |||||||
M35.2 | Behçet's disease Latin: Morbus Behcet | |||||||
M35.3 | Polymyalgia rheumatica Latin: Polymyalgia rheumatica | |||||||
Excludes: | polymyalgia rheumatica with giant cell arteritis (M31.5) | |||||||
M35.4 | Diffuse (eosinophilic) fasciitis Latin: Fasciitis diffusa (eosinophilica) | |||||||
M35.5 | Multifocal fibrosclerosis
Latin: Fibrosclerosis multifocalis | |||||||
M35.6 | Relapsing panniculitis [Weber-Christian] Latin: Panniculitis recidiva (Weber-Christian) | |||||||
Excludes: | panniculitis:
· NOS (M79.3) · lupus (L93.2) | |||||||
M35.7 | Hypermobility syndrome Latin: Syndroma hypermobilitatis | |||||||
Familial ligamentous laxity | ||||||||
Excludes: | Ehlers-Danlos syndrome
(Q79.6) ligamentous laxity NOS (M24.2) | |||||||
M35.8 | Other specified systemic involvement of connective tissue
Latin: Morbi textus connexivi systemici alii, specificati | |||||||
M35.9 | Systemic involvement of connective tissue, unspecified Latin: Morbus textus connexivi systemicus alius, non specificatus | |||||||
Autoimmune disease (systemic) NOS Collagen (vascular) disease NOS |
M36* | Systemic disorders of connective tissue in diseases classified elsewhere Latin: Morbi textus connexivi systemici in morbis aliis | |||||||
Excludes: | arthropathies in diseases classified elsewhere (M14.-*) | |||||||
M36.0* | Dermato(poly)myositis in neoplastic disease
(C00-D48+) Latin: Dermato (poly) myositis neoplasmosa (C00-D48+) | |||||||
M36.1* | Arthropathy in neoplastic disease (C00-D48+) Latin: Arthropathia neoplasmosa (C00-D48+) | |||||||
Arthropathy in:
· leukaemia (C91-C95+) · malignant histiocytosis (C96.1+) · multiple myeloma (C90.0+) | ||||||||
M36.2* | Haemophilic arthropathy (D66-D68+) Latin: Arthropathia haemophilica (D66-D68+) | |||||||
M36.3* | Arthropathy in other blood disorders (D50-D76+) Latin: Arthropathia in morbis sanguinis aliis (D50-D76+) | |||||||
Excludes: | arthropathy in Henoch(-Schönlein) purpura (M36.4*) | |||||||
M36.4* | Arthropathy in hypersensitivity reactions classified elsewhere Latin: Arthropathia allergica, alia | |||||||
Arthropathy in Henoch(-Schönlein) purpura (D69.0+) | ||||||||
M36.8* | Systemic disorders of connective tissue in other diseases classified elsewhere Latin: Morbi textus connexivi systemici in morbis aliis | |||||||
Systemic disorders of connective tissue in: · hypogammaglobulinaemia (D80.-+) · ochronosis (E70.2+) |
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