A00-B99 C00-D48D50-D89 E00-E90 F00-F99 G00-G99 H00-H59 H60-H95 I00-I99 J00-J99 K00-K93
L00-L99 M00-M99 N00-N99 O00-O99 P00-P96 Q00-Q99 R00-R99 S00-T98 V01-Y98 Z00-Z99 U00-U99

N00-N08 Glomerular diseases






Chapter XIV

Diseases of the genitourinary system
(N00-N99)

Glomerular diseases
(N00-N08)

Use additional code, if desired, to identify external cause (Chapter XX) or presence of renal failure (N17-N19).


Excludes:
*hypertensive renal disease (I12.-)

The following fourth-character subdivisions classify morphological changes and are for use with categories N00-N07. Subdivisions .0-.8 should not normally be used unless these have been specifically identified (e.g. by renal biopsy or autopsy). The three-character categories relate to clinical syndromes.

.0Minor glomerular abnormality
Latin: laesiones glomerulares minores
Minimal change lesion
.1Focal and segmental glomerular lesions
Latin: glomerulonephritis focalis et segmentalis
Focal and segmental:
· hyalinosis
· sclerosis
Focal glomerulonephritis
.2 Diffuse membranous glomerulonephritis
Latin: glomerulonephritis membranosa difusa
.3Diffuse mesangial proliferative glomerulonephritis
Latin: glomerulonephritis mesangioproliferativa difusa
.4 Diffuse endocapillary proliferative glomerulonephritis
Latin: glomerulonephritis endocapilaris proliferativa difusa
.5 Diffuse mesangiocapillary glomerulonephritis
Latin: glomerulonephritis mesangiocapilaris difusa
Membranoproliferative glomerulonephritis, types 1 and 3, or NOS
.6Dense deposit disease
Latin: glomerulonephritis membranoproliferativa typus 2
Membranoproliferative glomerulonephritis, type 2
.7Diffuse crescentic glomerulonephritis
Latin: glomerulonephritis extracapillaris
Extracapillary glomerulonephritis
.8Other
Latin: glomerulonephritis proliferativa NOS
Proliferative glomerulonephritis NOS
.9 Unspecified
Latin: glomerulonephritis, non specificata
N00Acute nephritic syndrome
Latin: Syndroma nephritica acuta
[See before N00 for subdivisions]
Includes:acute:
· glomerular disease
· glomerulonephritis
· nephritis
· renal disease NOS
Excludes:acute infectious tubulo-interstitial nephritis (N10)
nephritic syndrome NOS (N05.-)
N01 Rapidly progressive nephritic syndrome
Latin: Syndroma nephritica progressiva peracuta
[See before N00 for subdivisions]
Includes:rapidly progressive:
· glomerular disease
· glomerulonephritis
· nephritis
Excludes:nephritic syndrome NOS (N05.-)
N02Recurrent and persistent haematuria
Latin: Haematuria recidiva et persistens
[See before N00 for subdivisions]
Includes:haematuria:
· benign (familial)(of childhood)
· with morphological lesion specified in .0-.8 before N00.-
Excludes: haematuria NOS (R31)
N03Chronic nephritic syndrome
Latin: Syndroma nephritica chronica
[See before N00 for subdivisions]
Includes:chronic:
· glomerular disease
· glomerulonephritis
· nephritis
· renal disease NOS
Excludes:chronic tubulo-interstitial nephritis (N11.-)
diffuse sclerosing glomerulonephritis (N18.-)
nephritic syndrome NOS (N05.-)
N04Nephrotic syndrome
Latin: Syndroma nephroticum
[See before N00 for subdivisions]
Includes:congenital nephrotic syndrome
lipoid nephrosis
N05Unspecified nephritic syndrome
Latin: Syndroma nephritica non specificata
[See before N00 for subdivisions]
Includes:glomerular disease
glomerulonephritis
nephritis
}
}
}
NOS
nephropathy NOS and renal disease NOS with morphological lesion specified in .0-.8 before N00.-
Excludes: nephropathy NOS with no stated morphological lesion (N28.9)
renal disease NOS with no stated morphological lesion (N28.9)
tubulo-interstitial nephritis NOS (N12)
N06Isolated proteinuria with specified morphological lesion
Latin: Proteinuria cum laesione morphologica specificata
[See before N00 for subdivisions]
Includes:proteinuria (isolated)(orthostatic)(persistent) with morphological lesion specified in .0-.8 before N00.-
Excludes:proteinuria:
· NOS (R80)
· Bence Jones (R80)
· gestational (O12.1)
· isolated NOS (R80)
· orthostatic NOS (N39.2)
· persistent NOS (N39.1)
N07Hereditary nephropathy, not elsewhere classified
Latin: Nephropathia hereditaria
[See before N00 for subdivisions]
Excludes:Alport's syndrome (Q87.8)
hereditary amyloid nephropathy (E85.0)
nail patella syndrome (Q87.2)
non-neuropathic heredofamilial amyloidosis (E85.0)
N08*Glomerular disorders in diseases classified elsewhere
Latin: Glomerulonephropathia in morbis aliis
Includes: nephropathy in diseases classified elsewhere
Excludes:renal tubulo-interstitial disorders in diseases classified elsewhere (N16.-*)
N08.0*Glomerular disorders in infectious and parasitic diseases classified elsewhere
Latin: Glomerulonephropathia in morbis infectivis et morbis parasitariis
Glomerular disorders in:
· Plasmodium malariae malaria (B52.0+)
· mumps (B26.8+)
· schistosomiasis [bilharziasis] (B65.-+)
· septicaemia (A40-A41+)
· strongyloidiasis (B78.-+)
· syphilis (A52.7+)
N08.1*Glomerular disorders in neoplastic diseases
Latin: Glomerulonephropathia neoplastica
Glomerular disorders in:
· multiple myeloma (C90.0+)
· Waldenström's macroglobulinaemia (C88.0+)
N08.2*Glomerular disorders in blood diseases and disorders involving the immune mechanism
Latin: Glomerulonephropathia in morbis sanguinis et disordines systematis imunologicis
Glomerular disorders in:
· cryoglobulinaemia (D89.1+)
· disseminated intravascular coagulation [defibrination syndrome] (D65+)
· haemolytic-uraemic syndrome (D59.3+)
· Henoch(-Schönlein) purpura (D69.0+)
· sickle-cell disorders (D57.-+)
N08.3*Glomerular disorders in diabetes mellitus (E10-E14+ with common fourth character .2)
Latin: Glomerulonephropathia diabetica (E10-E14+)
N08.4*Glomerular disorders in other endocrine, nutritional and metabolic diseases
Latin: Glomerulonephropathia in morbis glandularum endocrinarum nutritionis et metabolismi
Glomerular disorders in:
· amyloidosis (E85.-+)
· Fabry(-Anderson) disease (E75.2+)
· lecithin cholesterol acyltransferase deficiency (E78.6+)
N08.5*Glomerular disorders in systemic connective tissue disorders
Latin: Glomerulonephropathia in morbis textus connexivi systematicis
Glomerular disorders in:
· Goodpasture's syndrome (M31.0+)
· microscopic polyangiitis (M31.7+)
· systemic lupus erythematosus (M32.1+)
· thrombotic thrombocytopenic purpura (M31.1+)
· Wegener's granulomatosis (M31.3+)
N08.8*Glomerular disorders in other diseases classified elsewhere
Latin: Glomerulonephropathia in morbis aliis
Glomerular disorders in subacute bacterial endocarditis (I33.0+)


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