Chapter XIV
Diseases of the genitourinary system
(N00-N99)
Glomerular diseases
(N00-N08)
Use additional code, if desired, to identify external cause (Chapter XX) or presence of renal failure (N17-N19).
Excludes:
*hypertensive renal disease (I12.-)
The following fourth-character subdivisions classify morphological changes and are for use with categories N00-N07. Subdivisions .0-.8 should not normally be used unless these have been specifically identified (e.g. by renal biopsy or autopsy). The three-character categories relate to clinical syndromes.
.0 | Minor glomerular abnormality Latin: laesiones glomerulares minores |
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Minimal change lesion | ||||||||
.1 | Focal and segmental glomerular lesions Latin: glomerulonephritis focalis et segmentalis | |||||||
Focal and segmental: · hyalinosis · sclerosis Focal glomerulonephritis |
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.2 | Diffuse membranous glomerulonephritis Latin: glomerulonephritis membranosa difusa | |||||||
.3 | Diffuse mesangial proliferative glomerulonephritis Latin: glomerulonephritis mesangioproliferativa difusa | |||||||
.4 | Diffuse endocapillary proliferative glomerulonephritis
Latin: glomerulonephritis endocapilaris proliferativa difusa | |||||||
.5 | Diffuse mesangiocapillary glomerulonephritis Latin: glomerulonephritis mesangiocapilaris difusa | |||||||
Membranoproliferative glomerulonephritis, types 1 and 3, or NOS | ||||||||
.6 | Dense deposit disease Latin: glomerulonephritis membranoproliferativa typus 2 | |||||||
Membranoproliferative glomerulonephritis, type 2 | ||||||||
.7 | Diffuse crescentic glomerulonephritis Latin: glomerulonephritis extracapillaris | |||||||
Extracapillary glomerulonephritis | ||||||||
.8 | Other Latin: glomerulonephritis proliferativa NOS | |||||||
Proliferative glomerulonephritis NOS | ||||||||
.9 | Unspecified Latin: glomerulonephritis, non specificata |
N00 | Acute nephritic syndrome Latin: Syndroma nephritica acuta | |||||||
[See before N00 for subdivisions] | ||||||||
Includes: | acute: · glomerular disease · glomerulonephritis · nephritis · renal disease NOS | |||||||
Excludes: | acute infectious tubulo-interstitial nephritis (N10) nephritic syndrome NOS (N05.-) |
N01 | Rapidly progressive nephritic syndrome Latin: Syndroma nephritica progressiva peracuta | |||||||
[See before N00 for subdivisions] | ||||||||
Includes: | rapidly progressive: · glomerular disease · glomerulonephritis · nephritis | |||||||
Excludes: | nephritic syndrome NOS (N05.-) |
N02 | Recurrent and persistent haematuria Latin: Haematuria recidiva et persistens | |||||||
[See before N00 for subdivisions] | ||||||||
Includes: | haematuria: · benign (familial)(of childhood) · with morphological lesion specified in .0-.8 before N00.- | |||||||
Excludes: | haematuria NOS (R31) |
N03 | Chronic nephritic syndrome Latin: Syndroma nephritica chronica | |||||||
[See before N00 for subdivisions] | ||||||||
Includes: | chronic: · glomerular disease · glomerulonephritis · nephritis · renal disease NOS | |||||||
Excludes: | chronic tubulo-interstitial nephritis (N11.-) diffuse sclerosing glomerulonephritis (N18.-) nephritic syndrome NOS (N05.-) |
N04 | Nephrotic syndrome Latin: Syndroma nephroticum | |||||||
[See before N00 for subdivisions] | ||||||||
Includes: | congenital nephrotic syndrome
lipoid nephrosis |
N05 | Unspecified nephritic syndrome Latin: Syndroma nephritica non specificata | |||||||
[See before N00 for subdivisions] | ||||||||
Includes: | glomerular disease glomerulonephritis nephritis | } } } | NOS | |||||
nephropathy NOS and renal disease NOS with morphological lesion specified in .0-.8 before N00.- | ||||||||
Excludes: | nephropathy NOS with no stated morphological lesion (N28.9) renal disease NOS with no stated morphological lesion (N28.9) tubulo-interstitial nephritis NOS (N12) |
N06 | Isolated proteinuria with specified morphological lesion
Latin: Proteinuria cum laesione morphologica specificata | |||||||
[See before N00 for subdivisions] | ||||||||
Includes: | proteinuria (isolated)(orthostatic)(persistent) with morphological lesion specified in .0-.8 before N00.- | |||||||
Excludes: | proteinuria: · NOS (R80) · Bence Jones (R80) · gestational (O12.1) · isolated NOS (R80) · orthostatic NOS (N39.2) · persistent NOS (N39.1) |
N07 | Hereditary nephropathy, not elsewhere classified Latin: Nephropathia hereditaria | |||||||
[See before N00 for subdivisions] | ||||||||
Excludes: | Alport's syndrome (Q87.8) hereditary amyloid nephropathy (E85.0) nail patella syndrome (Q87.2) non-neuropathic heredofamilial amyloidosis (E85.0) |
N08* | Glomerular disorders in diseases classified elsewhere Latin: Glomerulonephropathia in morbis aliis | |||||||
Includes: | nephropathy in diseases classified elsewhere | |||||||
Excludes: | renal tubulo-interstitial disorders in diseases classified elsewhere (N16.-*) | |||||||
N08.0* | Glomerular disorders in infectious and parasitic diseases classified elsewhere
Latin: Glomerulonephropathia in morbis infectivis et morbis parasitariis | |||||||
Glomerular disorders in: · Plasmodium malariae malaria (B52.0+) · mumps (B26.8+) · schistosomiasis [bilharziasis] (B65.-+) · septicaemia (A40-A41+) · strongyloidiasis (B78.-+) · syphilis (A52.7+) | ||||||||
N08.1* | Glomerular disorders in neoplastic diseases Latin: Glomerulonephropathia neoplastica | |||||||
Glomerular disorders in: · multiple myeloma (C90.0+) · Waldenström's macroglobulinaemia (C88.0+) | ||||||||
N08.2* | Glomerular disorders in blood diseases and disorders involving the immune mechanism Latin: Glomerulonephropathia in morbis sanguinis et disordines systematis imunologicis | |||||||
Glomerular disorders in: · cryoglobulinaemia (D89.1+) · disseminated intravascular coagulation [defibrination syndrome] (D65+) · haemolytic-uraemic syndrome (D59.3+) · Henoch(-Schönlein) purpura (D69.0+) · sickle-cell disorders (D57.-+) | ||||||||
N08.3* | Glomerular disorders in diabetes mellitus (E10-E14+ with common fourth character .2) Latin: Glomerulonephropathia diabetica (E10-E14+) | |||||||
N08.4* | Glomerular disorders in other endocrine, nutritional and metabolic diseases Latin: Glomerulonephropathia in morbis glandularum endocrinarum nutritionis et metabolismi | |||||||
Glomerular disorders in: · amyloidosis (E85.-+) · Fabry(-Anderson) disease (E75.2+) · lecithin cholesterol acyltransferase deficiency (E78.6+) | ||||||||
N08.5* | Glomerular disorders in systemic connective tissue disorders Latin: Glomerulonephropathia in morbis textus connexivi systematicis | |||||||
Glomerular disorders in: · Goodpasture's syndrome (M31.0+) · microscopic polyangiitis (M31.7+) · systemic lupus erythematosus (M32.1+) · thrombotic thrombocytopenic purpura (M31.1+) · Wegener's granulomatosis (M31.3+) | ||||||||
N08.8* | Glomerular disorders in other diseases classified elsewhere Latin: Glomerulonephropathia in morbis aliis | |||||||
Glomerular disorders in subacute bacterial endocarditis (I33.0+) |
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